Statistics and Associations
- Most common hereditary endothelial (deep) corneal dystrophy
- Strong female predilection
- Typically develops in fourth to fifth decade of life with gradual progression
- Leads to decreased, fluctuating vision usually worse in the morning
- Vision decrease secondary to corneal swelling
Management
- Generally no treatment until substantial vision decrease
- Endothelial keratoplasty is the main surgical intervention